Analysis of inner ear anomalies in unilateral congenital aural Atresia combined with Microtia

Euyhyun Park, Gijeong Lee, Hak Hyun Jung, Gi Jung Im

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    6 Citations (Scopus)

    Abstract

    Objectives. The aim of this study was to analyze the incidence of inner ear anomalies in patients with unilateral congenital aural atresia (CAA) combined with microtia. Methods. We retrospectively reviewed 61 patients with unilateral CAA combined with microtia who underwent high-resolution temporal bone computed tomography (TBCT) and hearing examination. Inner ear anomalies were analyzed using TBCT and evaluated according to the Jahrsdoerfer grading system, Marx classification, and extent of inferior displacement of the mastoid tegmen. Results. Inner ear anomalies were observed in 14 patients (23.0%). Lateral semicircular canal (LSCC) dysplasia was the most common inner ear anomaly, with an incidence of 16.4%. The incidence was significantly higher on the pathologic side than on the unaffected side (P =0.002). All vascular anomalies were observed in the high-riding jugular bulb, with an incidence of 24.6%. The incidence was significantly higher on the pathologic side than on the unaffected side (P<0.001). LSCC dysplasia was significantly more common in patients with a lower Jahrsdoerfer score (odds ratio, 0.66; P =0.004). Conclusion. The incidence of inner ear anomalies was relatively high in patients with unilateral CAA combined with microtia; LSCC dysplasia was the most common anomaly and the probability of coexistence was higher in patients with a lower Jahrsdoerfer score.

    Original languageEnglish
    Pages (from-to)176-180
    Number of pages5
    JournalClinical and Experimental Otorhinolaryngology
    Volume12
    Issue number2
    DOIs
    Publication statusPublished - 2019 May

    Bibliographical note

    Funding Information:
    This research was supported by the Basic Science Research Program through the National Research Foundation of Korea (NRF) funded by Korea Evaluation Institute of Industrial Technology (R1621961), Korea Health Industry Development Institute (R1606511) and Korea University research grant (K1609821, Q1620561), Seoul, Republic of Korea.

    Publisher Copyright:
    © 2019 by Korean Society of Otorhinolaryngology-Head and Neck Surgery.

    Keywords

    • Anomalies
    • Aural Atresia
    • Congenital
    • Congenital Microtia
    • Inner Ear
    • Semicircular Canals

    ASJC Scopus subject areas

    • Surgery
    • Otorhinolaryngology

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