Moyamoya disease in a child with previous acute necrotizing encephalopathy

Taik Kun Kim, Baik Lin Eun, Sang Hoon Cha, Kyoo Byung Chung, Jung Hyuck Kim, Baek Hyun Kim, Hwan Hoon Chung

    Research output: Contribution to journalArticlepeer-review

    5 Citations (Scopus)


    A previously healthy 24-day-old boy presented with a 2-day history of fever and had a convulsion on the day of admission. MRI showed abnormal signal in the thalami, caudate nuclei and central white matter. Acute necrotising encephalopathy was diagnosed, other causes having been excluded after biochemical and haematological analysis of blood, urine and CSF. He recovered, but with spastic quadriparesis. At the age of 28 months, he suffered sudden deterioration of consciousness and motor weakness of his right limbs. MRI was consistent with an acute cerebrovascular accident. Angiography showed bilateral middle cerebral artery stenosis or frank occlusion with numerous lenticulostriate collateral vessels consistent with moyamoya disease.

    Original languageEnglish
    Pages (from-to)644-647
    Number of pages4
    JournalPediatric Radiology
    Issue number9
    Publication statusPublished - 2003 Sept 1


    • Acute necrotising encephalopathy
    • Brain moyamoya
    • Child
    • Head
    • MRI

    ASJC Scopus subject areas

    • Pediatrics, Perinatology, and Child Health
    • Radiology Nuclear Medicine and imaging


    Dive into the research topics of 'Moyamoya disease in a child with previous acute necrotizing encephalopathy'. Together they form a unique fingerprint.

    Cite this